β-thalassemia
发布时间：2023-03-22 22:08:39
浏览次数：232
β-thalassemia
β 型地中海贫血
英文解释
β-thalasse major causes hemolytic anemia, poor growth, and skeletal abnormalities during infancy.Affected children will require regular lifelong blood transfusions.Beta thalassemia intermedia is less severe than beta thalassemia major and may require episodic blood transfusions.Transfusion-dependent patients will develop iron overload and require chelation therapy to remove the excess iron.
中文解释
β 型地中海贫血 (β-thalasse) 主要导致溶血性贫血、生长不良和婴儿时期的骨骼异常。受影响的儿童将需要终身定期输血。中间型地中海贫血的严重程度低于重度地中海贫血，可能需要间歇性输血。依赖输血的患者会出现铁超载，需要螯合治疗来清除多余的铁。
参考文献
[1]. Muncie HL Jr, Campbell J. Alpha and betathalassemia. Am Fam Physician. 2009 Aug 15;80(4):339-44.
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